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Documento descargado de http://www.elsevier.es el 20/06/2016.

Copia para uso personal, se prohíbe la transmisión de este documento por cualquier medio o formato.

Perinatol Reprod Hum. 2015;29(3):122-129

P erinatología
Y R EPRODUCCIÓN HUMANA
www.elsevier.es/rprh

REVISIÓN

Reemplazo estrogénico en pacientes con síndrome


de Turner

F. Pérez Bueno*, J.R. Aguilera Pérez y P. Garza Ríos

Coordinación de Peri-Posmenopausia, Instituto Nacional de Perinatología, México D.F., México

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3XEHUWDG cromosoma X, que ocurre un 1 caso por cada 2,000 a 2,500 mujeres nacidas vivas. Se asocia
(VWUyJHQRV JHQHUDOPHQWHFRQWDOODEDMDGLVJHQHVLDJRQDGDO\QLYHOHVFLUFXODQWHVLQVXÀFLHQWHVGHHVWHURL-
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Síndrome de Turner; QDOGHUHHPSOD]R 7+5 HQODDGROHVFHQWHHVD~QXQWHPDFRQWURYHUVLDO/DWHUDSLDFRQHVWUy-
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reciente.
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KEYWORDS Estrogen replacement in women with Turner’s syndrome


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* Autor para correspondencia.


Correo electrónico:ÁRUBSE#\DKRRFRPP[ )3pUH]%XHQR 
0187-5337/ © 2015 Instituto Nacional de Perinatología Isidro Espinosa de los Reyes. Publicado por Masson Doyma México S.A. Este es un artículo Open
Access bajo la licencia CC BY-NC-ND (http://creativecommons.org/licenses/by-nc-nd/4.0/).
Documento descargado de http://www.elsevier.es el 20/06/2016. Copia para uso personal, se prohíbe la transmisión de este documento por cualquier medio o formato.

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tipos que se encuentran en el ST son mosaicismos con otras
Historia y terminología OtQHDVFHOXODUHVWDOHVFRPR;;R;<y;;</DV
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GURFDUDFWHUL]DGRSRUHVWDWXUDEDMDDXVHQFLDGHFDUDFWHUHV mosoma X, deleciones, anillos o translocaciones.
VH[XDOHVIHPHQLQRVpterigium colli\cubitus valguspOFRQ- 3DFLHQWHVFRQFDULRWLSR;WLHQHQPiVFDUDFWHUtVWLFDV
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de uno de los cromosomas X en las pacientes con síndrome HQHOGHORVFDVRV\DTXHFXDQGRHVWHFURPRVRPDHVWi
de Turner. SUHVHQWHH[LVWHXQULHVJRLQFUHPHQWDGRGHGHGHVD-
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Documento descargado de http://www.elsevier.es el 20/06/2016. Copia para uso personal, se prohíbe la transmisión de este documento por cualquier medio o formato.

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Documento descargado de http://www.elsevier.es el 20/06/2016. Copia para uso personal, se prohíbe la transmisión de este documento por cualquier medio o formato.

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El tratamiento de las pacientes con ST requiere la valora- QDU/+\)6+SDUDH[FOXLUPDGXUDFLyQWDUGtD
FLyQ\VHJXLPLHQWRSHULyGLFRDGLIHUHQWHVHGDGHV$GHPiV /DIRUPXODFLyQRSWLPDGHHVWUyJHQRVGRVLVYtDGHDGPL-
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Documento descargado de http://www.elsevier.es el 20/06/2016. Copia para uso personal, se prohíbe la transmisión de este documento por cualquier medio o formato.

126 )3pUH]%XHQRHWDO

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Documento descargado de http://www.elsevier.es el 20/06/2016. Copia para uso personal, se prohíbe la transmisión de este documento por cualquier medio o formato.

5HHPSOD]RHVWURJpQLFRHQSDFLHQWHVFRQVtQGURPHGH7XUQHU 

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Documento descargado de http://www.elsevier.es el 20/06/2016. Copia para uso personal, se prohíbe la transmisión de este documento por cualquier medio o formato.

128 )3pUH]%XHQRHWDO

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GHUDGLFDOHVOLEUHVTXHSRWHQFLDUtDQHODXPHQWRGHORVVXV- WUXDFLRQHVTXHHQPXFKDVVRFLHGDGHVGHVGHXQSXQWRGH
tratos de renina circulantes. YLVWDFXOWXUDOVHUtDHOSLODUVXIHPLQHLGDG
Pacientes que presenten intolerancia a la lactosa son sus- 6HGHEHKDFHUSUHYHQFLyQGHHQIHUPHGDGHVFDUGLRYDVFX-
FHSWLEOHVGHVHUWUDWDGDVFRQYtDVDOWHUQDWLYDVDODRUDO\D lares, reducción de la mortalidad por causa cardiovascular
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